katabolizm aminokwasów

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Question Answer
Asparagina
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Asparagina (Asparaginaza) -> Asparaginian (Aminotransferaza) -> Szczawiooctan
Glutamina
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Glutamina(Glutaminaza) -> Glutaminian (Dehydrogenaza glut) -> alfa ketoglutaran
Prolina
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Prolina (utl) -> glutaminian -> alfa ketoglutaran
Arginina
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Arginina (Arginaza) -> ornityna -> alfa ketoglutaran
Histydyna
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Histydyna (Histydaza) -> kw urokanowy -> N-formimino glutaminian -> Glutaminian -> alfa ketoglutaran
Alanina
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Transaminacja -> pirogronian
Seryna
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Seryna (Dehydrataza serynowa) -> pirogronian / seryna (hydroksymetylotransferwza serynowa) -> glicyna
Glicyna
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dekarboksylaza serynowa -> do CO2 albo przez seryne do pirogronianu
Cysteina
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desulfuryzacja -> pirogronian
Treonina
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Dehydrataza treoninowa -> alfa keto maslan -> propionyloCoA —-> bursztynyloCoA, pirogronian
Fenyloalanina
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Fenyloalanina (hydroksylaza fenyloalaniny) -> tyrozyna -> fumaran + acetooctan
Metionina
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met (adenozylotransferaza metioninowa) -> SAM (metylotransferaza) -> SAH (Hydrolaza) -> homocysteina (syntaza cystationinowa) -> cystationina (cystationinaza) -> alfa ketomaslan (oks dekarboksylacja) -> propionyloCoA -> bursztynyloCoA
izoleucyna
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AcetyloCoA i propionyloCoA -> metylomalonyloCoA -> bursztynyloCoA
Walina
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propionyloCoA -> metylomalonyloCoA -> bursztynyloCoA
Tryptofan *
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Alanina i acetoacetyloCoA
Leucyna*
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acetyloCoA i acetooctan
Lizyna *
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acetoacetyloCoA

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